منابع مشابه
Erythropoietin in polycystic kidneys.
Erythropoietin (EPO) formation in kidneys of 18 patients with autosomal dominant polycystic kidney disease (ADPKD) was investigated. In 12 patients on hemodialysis and in 6 patients with preterminal renal failure serum, EPO was 29 +/- 7 and 16 +/- 1.5 mU/ml and hemoglobin concentrations were 11.0 +/- 0.6 and 12.7 +/- 1.2 g/dl, respectively. Cyst fluid from a total of 357 renal cysts was obtaine...
متن کاملGene profiling of polycystic kidneys.
BACKGROUND While the genetic basis of autosomal dominant polycystic kidney disease (ADPKD) has been clearly established, the pathogenesis of renal failure in ADPKD remains elusive. Cyst formation originates from proliferating renal tubular epithelial cells that de-differentiate. Fluid secretion with cyst expansion and reactive changes in the extracellular matrix composition combined with increa...
متن کاملOral-facial-digital syndrome, with polycystic kidneys and liver: pathological and cytogenetic studies.
In 1954 Papillon-Leage and Psaume (I954a, b) described 8 patients with a syndrome characterized by congenital anomalies of the face, oral cavity, and digits. Since then, several groups of patients have been reported (Gorlin, Anderson, and Scott, I96I; Ruess, Pruzansky, Lis, and Patau, I962; Gorlin and Psaume, I962; Kaplan, Vaharu, Voorhess, and Gardner, I962; Kushnick, Massa, and Baukema, I963;...
متن کاملAssociation of von Recklinghausen's neurofibromatosis with adult polycystic disease of kidneys and liver.
Introduction Von Recklinghausen's neurofibromatosis and adult polycystic disease of the kidneys (APDK) are both heredofamilial disorders (Preiser and Davenport, 1918; Dalgaard, 1971) although sporadic cases also occur (Wander and Dsgupta, 1977; Hatfield and Pfister, 1972). Both the conditions are known to occur in association with a number of other hereditary disorders (Dalgaard, 1971; Koch, 19...
متن کاملLaminin 5 Regulates Polycystic Kidneys Cell Proliferation and Cyst Formation
LAMININ 5 REGULATES POLYCYSTIC KIDNEYS CELL PROLIFERATION AND CYST FORMATION Dominique Joly, Sophie Berissi, Amélie Bertrand, Laetitia Strehl, Natacha Patey and Bertrand Knebelmann. From Université Paris-Descartes, Faculté de Médecine ; Inserm U813; AP-HP Hôpital Necker-Enfants-Malades, Paris, France Address correspondance to : Bertrand KNEBELMANN, Department of Nephrology, Hôpital Necker-Enfan...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Annals of Surgery
سال: 1921
ISSN: 0003-4932
DOI: 10.1097/00000658-192101000-00010